Anti-HADHA Polyclonal Antibody
應(yīng)用 WB
稀釋比例WB 1:500-2000.
交叉反應(yīng)Human Mouse Rat

產(chǎn)品型號(hào)：K106618P

更新時(shí)間：2022-08-15

廠商性質(zhì)：生產(chǎn)廠家

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Anti-HADHA Polyclonal Antibody

英文名稱	Anti-HADHA Polyclonal Antibody
宿主	Rabbit
別名	HADHA;ECHA;GBP;HADH;LCEH;LCHAD;MTPA;TP-ALPHA
應(yīng)用	WB
稀釋比例	WB 1:500-2000.
交叉反應(yīng)	Human Mouse Rat
蛋白分子量	83kDa
Gene ID	3030
保存	Store at -20°C. Avoid freeze / thaw cycles.
儲(chǔ)存液	Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3.
純化方法	Affinity purification
亞型	IgG
免疫原	Recombinant protein of human HADHA
性狀	液體
Public Immunogen Range	Recombinant protein of human HADHA
Subcellular Locations	Cytoplasm
Swiss Prot	P40939
克隆類型	Polyclonal Antibody
背景資料	This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.